| Mitochondrial cristae shape determines respiratory chain supercomplexes assembly and respiratory efficiency S Cogliati, C Frezza, ME Soriano, T Varanita, R Quintana-Cabrera, ... Cell 155 (1), 160-171, 2013 | 1175 | 2013 |
| Supercomplex assembly determines electron flux in the mitochondrial electron transport chain E Lapuente-Brun, R Moreno-Loshuertos, R Acín-Pérez, A Latorre-Pellicer, ... Science 340 (6140), 1567-1570, 2013 | 880 | 2013 |
| NDUFA4 is a subunit of complex IV of the mammalian electron transport chain E Balsa, R Marco, E Perales-Clemente, R Szklarczyk, E Calvo, ... Cell metabolism 16 (3), 378-386, 2012 | 428 | 2012 |
| Induction of the mitochondrial NDUFA4L2 protein by HIF-1α decreases oxygen consumption by inhibiting Complex I activity D Tello, E Balsa, B Acosta-Iborra, E Fuertes-Yebra, A Elorza, Á Ordóñez, ... Cell metabolism 14 (6), 768-779, 2011 | 341 | 2011 |
| Culture of human mesenchymal stem cells at low oxygen tension improves growth and genetic stability by activating glycolysis ES J C Estrada, C Albo, A Benguría, A Dopazo, P López-Romero, L Carrera ... Cell Death Differ. 19 (5), 743–755, 2012 | 306 | 2012 |
| The CoQH2/CoQ ratio serves as a sensor of respiratory chain efficiency A Guaras, E Perales-Clemente, E Calvo, R Acín-Pérez, M Loureiro-Lopez, ... Cell reports 15 (1), 197-209, 2016 | 260 | 2016 |
| Disease-causing mitochondrial heteroplasmy segregated within induced pluripotent stem cell clones derived from a patient with MELAS CDL Folmes, A Martinez-Fernandez, E Perales-Clemente, X Li, ... Stem Cells 31 (7), 1298-1308, 2013 | 119 | 2013 |
| Allotopic expression of mitochondrial-encoded genes in mammals: achieved goal, undemonstrated mechanism or impossible task? E Perales-Clemente, P Fernandez-Silva, R Acín-Pérez, A Perez-Martos, ... Nucleic acids research 39 (1), 225-234, 2011 | 115 | 2011 |
| Restoration of electron transport without proton pumping in mammalian mitochondria E Perales-Clemente, MP Bayona-Bafaluy, A Pérez-Martos, A Barrientos, ... Proceedings of the National Academy of Sciences 105 (48), 18735-18739, 2008 | 94 | 2008 |
| Natural underlying mt DNA heteroplasmy as a potential source of intra‐person hi PSC variability E Perales‐Clemente, AN Cook, JM Evans, S Roellinger, F Secreto, ... The EMBO journal 35 (18), 1979-1990, 2016 | 88 | 2016 |
| Five entry points of the mitochondrially encoded subunits in mammalian complex I assembly E Perales-Clemente, E Fernández-Vizarra, R Acín-Pérez, N Movilla, ... Molecular and cellular biology 30 (12), 3038-3047, 2010 | 85 | 2010 |
| m. 3243A> G-induced mitochondrial dysfunction impairs human neuronal development and reduces neuronal network activity and synchronicity TMK Gunnewiek, EJH Van Hugte, M Frega, GS Guardia, K Foreman, ... Cell reports 31 (3), 2020 | 70* | 2020 |
| Metabolic regulation of redox status in stem cells E Perales-Clemente, CDL Folmes, A Terzic Antioxidants & redox signaling 21 (11), 1648-1659, 2014 | 67 | 2014 |
| Spot14/Mig12 heterocomplex sequesters polymerization and restrains catalytic function of human acetyl‐CoA carboxylase 2 S Park, IW Hwang, Y Makishima, E Perales‐Clemente, T Kato, ... Journal of Molecular Recognition 26 (12), 679-688, 2013 | 29 | 2013 |
| A new D‐galactose treatment monitoring index for PGM1‐CDG E Perales‐Clemente, K Liedtke, A Studinski, S Radenkovic, D Gavrilov, ... Journal of inherited metabolic disease 44 (5), 1263-1271, 2021 | 11 | 2021 |
| Quantification of etoposide hypersensitivity: a sensitive, functional method for assessing pluripotent stem cell quality FJ Secreto, X Li, AJ Smith, ES Bruinsma, E Perales-Clemente, S Oommen, ... Stem cells translational medicine 6 (10), 1829-1839, 2017 | 6 | 2017 |
| Engineering targeted deletions in the mitochondrial genome JM Campbell, E Perales-Clemente, H Ata, N Vidal-Folch, W Liu, KJ Clark, ... bioRxiv, 287342, 2018 | 4 | 2018 |
| Bilateral subdural hematomas and retinal hemorrhages mimicking nonaccidental trauma in a patient with D‐2‐hydroxyglutaric aciduria E Perales‐Clemente, AL Hewitt, AL Studinski, JM Tillema, WJ Laxen, ... JIMD reports 58 (1), 21-28, 2021 | 1 | 2021 |
| Brain-on-a-chip-a neurophysiological model of MELAS disease and comorbid psychopathology T Kozicz, T Klein-Gunnewiek, D Cassiman, T Nelson, R Rodenburg, ... European Journal Of Human Genetics 27, 1161-1162, 2019 | 1 | 2019 |
| Mitochondrial dysfunction impairs human neuronal development and reduces neuronal network activity and synchronicity EJH Van Hugte, M Frega, GS Guardia, K Foreman, D Panneman, ... | | 2019 |
